Synonym- Endothelial sarcoma of bone
Swings sarcoma is an
uncommon but highly malignant sarcoma arising from endothelial cells in the
bone marrow.
Age incidence- usually between 10 and 20 years.
Common sites- shaft of femur, tibia, fibula, humerus or clavicle.
Pathology:
The tumour tissue is soft
and vascular. As it expands it gradually destroys the bone substance. There is
striking reaction beneath the periosteum, where abundant new bone is formed in
successive layers. Macroscopically the tumour is lobuloted and often fairly
large. It may look Grey (like brain) or red (like red current jelly) if
hemorrhage occur into it. Microscopically, sheets of small dark polyhedral cell
with no regular arrangement and no ground substance are seen.
Clinical Feature:
1.
Pain- Often throbbing is character with rapidly increasing swelling
over the shaft of a long bone.
2.
Pyrexia, warm, tender swelling which is fusiform in shape and firm in
consistency.
Investigations:
1. X-ray a. Onion-peel appearance
b. Sunray appearance and codman’s traingles are
also present.
2. CT & MRI - Reveal
both osseous & extra osseous component of tumour.
3. Chest X-ray P/A view - Show pulmonary metastesis.
4. Radioisotope scan - Markedly in
creased uptake of the isotope in the region of the tumour.
5. FNAC.
Differential Diagnosis
1.
Subacute osteomyelitis
2.
Syphilitic osteoperiostitis
3.
Reticulur cell sarcoma
4.
Metastetic neuroblastoma.
Treatment:
The best results are achieved by a combination
of all three methods a course of preoperative chemotherapy; then wide excision
(or amputation) if the tumour is in a favorable site or radiotherapy followed
by local excision if it is less accessible and then a further course of
chemotherapy for 1 year.
0 Comments Received
Leave A Reply